A quantitative analytical standard guaranteed to meet MaxSpec? identity, purity, stability, and concentration specifications
货号:ajcx26288
CAS:N/A
分子式:C24H45D3NO4 • Cl
分子量：453.1
溶解度:N/A
纯度：98%
存储：Store at -20°C
库存：现货

Background:

Heptadecanoyl-L-carnitine-d₃is intended for use as an analytical standard for the quantification of heptadecanoyl-L-carnitine by GC- or LC-MS. Heptadecanoyl-L-carnitine is a long-chain acylcarnitine composed of heptadecanoic acid and L-carnitine . Levels of heptadecanoyl-L-carnitine are increased in dried blood spots from neonates with propionic or methylmalonic acidemias, inborn errors of metabolism characterized by a deficiency in the activity of propionyl-CoA carboxylase or L-methylmaolnyl-CoA mutase or its cofactor 5-deoxyadenosylcobalamin, respectively.¹

1.Malvagia, S., Haynes, C.A., Grisotto, L., et al.Heptadecanoylcarnitine (C17) a novel candidate biomarker for propionic and methylmalonic acidemias during expanded newborn screeningClin. Chim. Acta450342-348(2015)